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Ivemark Syndrome. A rare entity with specific anatomical features.

dc.contributoren-US
dc.creatorHrusca, Adrian; University of Medicine & Pharmacy " Iuliu Hatieganu" Cluj-Napoca Department of Pediatrics II
dc.creatorRachisan, Andreea Liana; University of Medicine & Pharmacy " Iuliu Hatieganu" Cluj-Napoca Department of Pediatrics II
dc.creatorLucian, Bogdan; Department of Pediatrics, Baia-Mare County Hospital, Romania
dc.creatorOprita, Simona; Department of Cardiology, Cluj-Napoca County Hospital, Cluj-Napoca, Romania
dc.creatorManole, Simona; Department of Radiology, Cluj-Napoca County Hospital, Cluj-Napoca, Romania
dc.creatorCainap, Simona; University of Medicine & Pharmacy " Iuliu Hatieganu" Cluj-Napoca Department of Pediatrics II
dc.date2015-01-30
dc.date.accessioned2019-11-11T18:27:52Z
dc.date.available2019-11-11T18:27:52Z
dc.identifierhttp://www.revistamedicadechile.cl/ojs/index.php/rmedica/article/view/3974
dc.identifier.urihttps://revistaschilenas.uchile.cl/handle/2250/111326
dc.descriptionIvemark syndrome (IS) is a rare embryological disorder which results from failure of development of the left-right asymmetry of organs. It is often associated with cardiac and other organ abnormalities, which are the usual causes of death in early neonatal life. We report a 3 months old girl with IS with dextrocardia, transposition of the great vessels, atrio-ventricular connection, total anomalous pulmonary venous drainage, a right atrial and right pulmonary isomerism, a midline liver, a midline gallbladder, asplenia, intestinal malrotation and vena cava anomalies. To our knowledge, complete right heterotaxia syndrome has been rarely described in literature. Lateralization defects such as situs inversus, asplenia or polysplenia due to defective left-right axis development are considered as defects of the primary developmental field. Therefore, additional malformations in IS can be synchronic defects in the primary developmental field rather than causally independent malformations.en-US
dc.format\\\"application/octet-stream\\\"
dc.languageeng
dc.publisherRevista Médica de Chilees-ES
dc.relationhttp://www.revistamedicadechile.cl/ojs/index.php/rmedica/article/view/3974/911
dc.relationhttp://www.revistamedicadechile.cl/ojs/index.php/rmedica/article/downloadSuppFile/3974/16539
dc.relationhttp://www.revistamedicadechile.cl/ojs/index.php/rmedica/article/downloadSuppFile/3974/16540
dc.relationhttp://www.revistamedicadechile.cl/ojs/index.php/rmedica/article/downloadSuppFile/3974/16541
dc.relationhttp://www.revistamedicadechile.cl/ojs/index.php/rmedica/article/downloadSuppFile/3974/16542
dc.relationhttp://www.revistamedicadechile.cl/ojs/index.php/rmedica/article/downloadSuppFile/3974/16543
dc.relationhttp://www.revistamedicadechile.cl/ojs/index.php/rmedica/article/downloadSuppFile/3974/16544
dc.relationhttp://www.revistamedicadechile.cl/ojs/index.php/rmedica/article/downloadSuppFile/3974/18503
dc.sourceRevista Médica de Chile; Vol. 143, núm. 3 (2015): MARZO 2015es-ES
dc.source0034-9887
dc.subjectCongenital abnormalities; Heterotaxy syndrome; Ivemark syndrome; Situs ambiguous with aspleniaen-US
dc.titleIvemark Syndrome. A rare entity with specific anatomical features.en-US
dc.typeinfo:eu-repo/semantics/article
dc.typeinfo:eu-repo/semantics/publishedVersion
dc.typees-ES


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